Abstract: [Abstract] Objective To explore the prevalence, cause and clinical features of Sj?gren’s Syndrome complicated with pulmonary arterial hypertension. Methods The data of 61 cases in my department with the diagnosis of pSS during November 2010 to April 2011 were collected. All the cases take ultrasonocardiograph. Results In this study, the prevalence of pSS-PAH is 16.4%. The occurrence of pulmonary arterial hypertension is associated with Raynaud’s phenomenon, dry cough, chest tightness or chest pain, progressive dyspnea, heart palpitations, interstitial lung disease or disease active. Conclusion pSS patients without clinical symptoms, they also should do UCG, which is important to early diagnosis and treatment.

Key words: pulmonary artrial hypertension, Sj?gren’s syndrome, color Doppler echocardiography, Raynaud’s phenomenon, interstitial lung disease