Abstract: Coronary artery origin abnormalities include a variety of congenital coronary vascular variations,The left main coronary artery opening in the right coronary sinus is a rare and prognostic coronary artery anomaly.The symptoms of angina, syncope and myocardial ischemia were present in this patient, but some patients had no clinical symptoms and died suddenly after strenuous exercise.How to understand the disease as early as possible early surgical treatment is the key.

Key words: children, anomalous origin of coronary artery, right coronary sinus