Abstract: Paraganglioma of the urinary bladder, which arises from the chromaffin tissue of the sympathetic nervous system in locations of the bladder, is also termed to as extra-adrenal pheochromocytomas. Bladder paraganglioma is a rare bladder tumor, however, the report of bladder paraganglioma co-existing with bladder urothelial carcinoma is even rare. We report one case of special bladder paraganglioma with bladder carcinoma. Herein we sought to review the literatures on praganglioma of the urinary bladder and bladder carcinoma in order to further illustrate the presentation, treatment options and outcomes of patients diagnosed with these tumors.

Key words: paraganglioma, urinary bladder neoplasms, ureteral neoplasms, case reports