Abstract: Objective The present study reports a patient with a rare acoustic neuroma that aroses from the cochlea. Methods In order to diagnose and treat, a detailed analysis is performed according to the case history, physical examination and radiographic findings {CT (computerized tomography) and MRI (magnetic resonance imaging) scanning}. And literature review. Results Some specialists discuss this case. Consequently, intralabyrinth acoustic neuroma is identified so that other possibilities are excluded. Surgical treatment is regarded as the optimal choice. Because the patient doesn’t agree with it, gamma knife (γ-knife) is used at last. Conclusions Intralabyrinth acoustic neuroma has no typical clinical symptoms, and gadolinium enhanced MRI examination is its best diagnostic tool. Early tumors confine to the labyrinth and no severe dizziness symptoms can be observed. If the patient has severe vertigo, or tumors spread out of the labyrinth, surgical resection of the tumors or the use of r-knife treatment should be applied.

Key words: Acoustic Neuroma, Acoustic, Intralabyrenth